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Leucinosis (MSUD)

Leucinosis is a hereditary metabolic disease, characterized by the inability of the individual affected to metabolize branched chain amino acids (leucine, isoleucine and valine).

Amino acids are the constituent units of proteins and are therefore daily taken as part of one’s diet. Individuals suffering from Leucinosis should follow a diet without amino acids which fail to metabolise (leucine, isoleucine and valine).

Given the impossibility of excluding these amino acids from natural proteins, the patient will, in general, have to follow a protein-free diet, supplemented with adequate protein substitutes (which do not contain leucine, isoleucine and valine).

PIAM, always attentive to the problems related to rare or low-prevalence diseases, offers a diversified range of specific protein substitutes for the proper nutritional management of patients suffering from Leucinosis, providing tailor-made solutions for all ages, from infancy to adulthood.