{"id":3516,"date":"2023-01-09T16:48:05","date_gmt":"2023-01-09T16:48:05","guid":{"rendered":"https:\/\/www.piamfarmaceutici.com\/patologia\/disturbo-dellossidazione-degli-acidi-grassi\/"},"modified":"2023-01-09T16:48:05","modified_gmt":"2023-01-09T16:48:05","slug":"disturbo-dellossidazione-degli-acidi-grassi","status":"publish","type":"patologia","link":"https:\/\/www.piamfarmaceutici.com\/en\/patologia\/disturbo-dellossidazione-degli-acidi-grassi\/","title":{"rendered":"Fatty acid oxidation disorders"},"content":{"rendered":"<p><span style=\"font-weight: 400;\">Inborn disorders of lipid metabolism that reduce the body&#8217;s ability to convert fat into energy <\/span><span style=\"font-weight: 400;\">are <\/span><span style=\"font-weight: 400;\">normally defined as fatty acid oxidation disorders and fall within the large family of Hereditary Metabolic Diseases (HMDs).<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Fatty acids are one of the main energy substrates for the body. When these are not efficiently metabolised to produce energy, there may be various problems for the body characterized by complex systemic clinical patterns and organ damage.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">The long-term treatment of patients with these diseases generally involves:<\/span><\/p>\n<ul>\n<li><span style=\"font-weight: 400;\"> avoiding prolonged fasting<\/span><\/li>\n<li><span style=\"font-weight: 400;\"> avoiding excessive muscle strain<\/span><\/li>\n<li><span style=\"font-weight: 400;\"> establishing a diet therapy based on small and frequent meals, rich in complex carbohydrates and low in fat.<\/span><\/li>\n<li><span style=\"font-weight: 400;\"> limiting the intake of long-chain fatty acids (LCT) and increasing the intake of medium-chain fatty acids (MCT). This dietary approach allows an adequate caloric intake to be reached, which, especially in children, would be impossible with only proteins and carbohydrates.<\/span><\/li>\n<\/ul>\n<p><span style=\"font-weight: 400;\">The treatment is, however, customized according to the needs of the individual patient.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">PIAM, always attentive to the particular needs of patients suffering from rare or low-prevalence diseases, is able to offer nutritional support therapies for patients suffering from fatty acid oxidation disorders.<\/span><\/p>\n","protected":false},"featured_media":3517,"template":"","categoria-patologia":[218],"class_list":["post-3516","patologia","type-patologia","status-publish","has-post-thumbnail","hentry","categoria-patologia-congenital-disorders-of-lipid-metabolism"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.8 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Fatty acid oxidation disorders - PIAM farmaceutici s.p.a<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.piamfarmaceutici.com\/en\/patologia\/disturbo-dellossidazione-degli-acidi-grassi\/\" \/>\n<meta property=\"og:locale\" content=\"en_US\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Fatty acid oxidation disorders - PIAM farmaceutici s.p.a\" \/>\n<meta property=\"og:description\" content=\"Inborn disorders of lipid metabolism that reduce the body&#8217;s ability to convert fat into energy are normally defined as fatty acid oxidation disorders and fall within the large family of Hereditary Metabolic Diseases (HMDs). Fatty acids are one of the main energy substrates for the body. 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