{"id":3507,"date":"2023-01-09T16:22:44","date_gmt":"2023-01-09T16:22:44","guid":{"rendered":"https:\/\/www.piamfarmaceutici.com\/patologia\/isovalerico-aciduria-iva\/"},"modified":"2023-01-27T11:48:27","modified_gmt":"2023-01-27T11:48:27","slug":"isovalerico-aciduria-iva","status":"publish","type":"patologia","link":"https:\/\/www.piamfarmaceutici.com\/en\/patologia\/isovalerico-aciduria-iva\/","title":{"rendered":"Isovaleric Aciduria (IVA)"},"content":{"rendered":"<p><span style=\"font-weight: 400;\">Isovaleric Aciduria is an inherited metabolic disease related to the metabolism of the amino acid leucine.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Amino acids are the constituent units of proteins and are therefore daily taken as part of one\u2019s diet. Individuals with Isovaleric Aciduria should follow a diet that does not contain the amino acid leucine, in order to minimize isovaleric acid formation.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Given the impossibility of excluding this amino acid from natural proteins, the patient, in general, should follow a protein-free diet, supplemented with adequate protein substitutes (without leucine).<\/span><\/p>\n<p><span style=\"font-weight: 400;\">PIAM, always attentive to the problems related to rare or low-prevalence diseases, offers a diversified range of specific protein substitutes for the correct nutritional management of patients affected by Isovaleric Aciduria, providing tailor-made solutions for all ages, from infancy to adulthood.<\/span><\/p>\n<p>&nbsp;<\/p>\n","protected":false},"featured_media":3508,"template":"","categoria-patologia":[215],"class_list":["post-3507","patologia","type-patologia","status-publish","has-post-thumbnail","hentry","categoria-patologia-inborn-errors-of-protein-metabolism"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.7 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Isovaleric Aciduria (IVA) - PIAM farmaceutici s.p.a<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.piamfarmaceutici.com\/en\/patologia\/isovalerico-aciduria-iva\/\" \/>\n<meta property=\"og:locale\" content=\"en_US\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Isovaleric Aciduria (IVA) - PIAM farmaceutici s.p.a\" \/>\n<meta property=\"og:description\" content=\"Isovaleric Aciduria is an inherited metabolic disease related to the metabolism of the amino acid leucine. 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