{"id":3504,"date":"2023-01-09T16:22:44","date_gmt":"2023-01-09T16:22:44","guid":{"rendered":"https:\/\/www.piamfarmaceutici.com\/patologia\/glutarico-aciduria-tipo-1-ga-1-2\/"},"modified":"2023-01-27T11:46:38","modified_gmt":"2023-01-27T11:46:38","slug":"glutarico-aciduria-tipo-1-ga-1-2","status":"publish","type":"patologia","link":"https:\/\/www.piamfarmaceutici.com\/en\/patologia\/glutarico-aciduria-tipo-1-ga-1-2\/","title":{"rendered":"Glutaric Aciduria type 1 (GA-1)"},"content":{"rendered":"<p><span style=\"font-weight: 400;\">Glutaric Aciduria is an inherited metabolic disease that involves the metabolism of three amino acids: lysine, hydroxylisine and tryptophan.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Amino acids are the constituent units of proteins and are therefore daily taken as part of one\u2019s diet. Individuals with Glutaric Aciduria type 1 should be on a lysine-free and low-tryptophan diet.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Given the impossibility of excluding these amino acids from natural proteins, the patient should, in general, follow a protein-free diet, supplemented with adequate protein substitutes (free from lysine and with a low tryptophan content). The treatment is, however, customized according to the needs of the individual patient.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">PIAM, always attentive to the problems related to rare or low-prevalence diseases, offers a diversified range of specific protein substitutes for the correct nutritional management of patients suffering from Glutaric Aciduria type 1, providing tailor-made solutions for all ages, from childhood up to adulthood.<\/span><\/p>\n<p>&nbsp;<\/p>\n","protected":false},"featured_media":3505,"template":"","categoria-patologia":[215],"class_list":["post-3504","patologia","type-patologia","status-publish","has-post-thumbnail","hentry","categoria-patologia-inborn-errors-of-protein-metabolism"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.7 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Glutaric Aciduria type 1 (GA-1) - PIAM farmaceutici s.p.a<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.piamfarmaceutici.com\/en\/patologia\/glutarico-aciduria-tipo-1-ga-1-2\/\" \/>\n<meta property=\"og:locale\" content=\"en_US\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Glutaric Aciduria type 1 (GA-1) - PIAM farmaceutici s.p.a\" \/>\n<meta property=\"og:description\" content=\"Glutaric Aciduria is an inherited metabolic disease that involves the metabolism of three amino acids: lysine, hydroxylisine and tryptophan. 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Given the impossibility of [&hellip;]\" \/>\n<meta property=\"og:url\" content=\"https:\/\/www.piamfarmaceutici.com\/en\/patologia\/glutarico-aciduria-tipo-1-ga-1-2\/\" \/>\n<meta property=\"og:site_name\" content=\"PIAM farmaceutici s.p.a\" \/>\n<meta property=\"article:modified_time\" content=\"2023-01-27T11:46:38+00:00\" \/>\n<meta property=\"og:image\" content=\"https:\/\/www.piamfarmaceutici.com\/wp-content\/uploads\/2023\/01\/glutarico_aciduria_tipo_1_GA-1-1-4.jpg\" \/>\n\t<meta property=\"og:image:width\" content=\"1920\" \/>\n\t<meta property=\"og:image:height\" content=\"1280\" \/>\n\t<meta property=\"og:image:type\" content=\"image\/jpeg\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Est. reading time\" \/>\n\t<meta name=\"twitter:data1\" content=\"1 minute\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\\\/\\\/schema.org\",\"@graph\":[{\"@type\":\"WebPage\",\"@id\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/en\\\/patologia\\\/glutarico-aciduria-tipo-1-ga-1-2\\\/\",\"url\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/en\\\/patologia\\\/glutarico-aciduria-tipo-1-ga-1-2\\\/\",\"name\":\"Glutaric Aciduria type 1 (GA-1) - PIAM farmaceutici s.p.a\",\"isPartOf\":{\"@id\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/#website\"},\"primaryImageOfPage\":{\"@id\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/en\\\/patologia\\\/glutarico-aciduria-tipo-1-ga-1-2\\\/#primaryimage\"},\"image\":{\"@id\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/en\\\/patologia\\\/glutarico-aciduria-tipo-1-ga-1-2\\\/#primaryimage\"},\"thumbnailUrl\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/wp-content\\\/uploads\\\/2023\\\/01\\\/glutarico_aciduria_tipo_1_GA-1-1-4.jpg\",\"datePublished\":\"2023-01-09T16:22:44+00:00\",\"dateModified\":\"2023-01-27T11:46:38+00:00\",\"breadcrumb\":{\"@id\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/en\\\/patologia\\\/glutarico-aciduria-tipo-1-ga-1-2\\\/#breadcrumb\"},\"inLanguage\":\"en-US\",\"potentialAction\":[{\"@type\":\"ReadAction\",\"target\":[\"https:\\\/\\\/www.piamfarmaceutici.com\\\/en\\\/patologia\\\/glutarico-aciduria-tipo-1-ga-1-2\\\/\"]}]},{\"@type\":\"ImageObject\",\"inLanguage\":\"en-US\",\"@id\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/en\\\/patologia\\\/glutarico-aciduria-tipo-1-ga-1-2\\\/#primaryimage\",\"url\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/wp-content\\\/uploads\\\/2023\\\/01\\\/glutarico_aciduria_tipo_1_GA-1-1-4.jpg\",\"contentUrl\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/wp-content\\\/uploads\\\/2023\\\/01\\\/glutarico_aciduria_tipo_1_GA-1-1-4.jpg\",\"width\":1920,\"height\":1280},{\"@type\":\"BreadcrumbList\",\"@id\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/en\\\/patologia\\\/glutarico-aciduria-tipo-1-ga-1-2\\\/#breadcrumb\",\"itemListElement\":[{\"@type\":\"ListItem\",\"position\":1,\"name\":\"Home\",\"item\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/en\\\/\"},{\"@type\":\"ListItem\",\"position\":2,\"name\":\"Glutaric Aciduria type 1 (GA-1)\"}]},{\"@type\":\"WebSite\",\"@id\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/#website\",\"url\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/\",\"name\":\"PIAM farmaceutici s.p.a\",\"description\":\"\",\"potentialAction\":[{\"@type\":\"SearchAction\",\"target\":{\"@type\":\"EntryPoint\",\"urlTemplate\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/?s={search_term_string}\"},\"query-input\":{\"@type\":\"PropertyValueSpecification\",\"valueRequired\":true,\"valueName\":\"search_term_string\"}}],\"inLanguage\":\"en-US\"}]}<\/script>\n<!-- \/ Yoast SEO plugin. -->","yoast_head_json":{"title":"Glutaric Aciduria type 1 (GA-1) - PIAM farmaceutici s.p.a","robots":{"index":"index","follow":"follow","max-snippet":"max-snippet:-1","max-image-preview":"max-image-preview:large","max-video-preview":"max-video-preview:-1"},"canonical":"https:\/\/www.piamfarmaceutici.com\/en\/patologia\/glutarico-aciduria-tipo-1-ga-1-2\/","og_locale":"en_US","og_type":"article","og_title":"Glutaric Aciduria type 1 (GA-1) - PIAM farmaceutici s.p.a","og_description":"Glutaric Aciduria is an inherited metabolic disease that involves the metabolism of three amino acids: lysine, hydroxylisine and tryptophan. 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