{"id":3501,"date":"2023-01-09T16:22:44","date_gmt":"2023-01-09T16:22:44","guid":{"rendered":"https:\/\/www.piamfarmaceutici.com\/patologia\/metilmalonico-aciduria-propionico-aciduria-mma-pa\/"},"modified":"2023-01-27T11:49:43","modified_gmt":"2023-01-27T11:49:43","slug":"metilmalonico-aciduria-propionico-aciduria-mma-pa","status":"publish","type":"patologia","link":"https:\/\/www.piamfarmaceutici.com\/en\/patologia\/metilmalonico-aciduria-propionico-aciduria-mma-pa\/","title":{"rendered":"Methylmalonic Aciduria \/ Propionic Aciduria (MMA \/ PA)"},"content":{"rendered":"<p><span style=\"font-weight: 400;\">Methylmalonic Aciduria and Propionic Aciduria are hereditary metabolic diseases related to the metabolism of some amino acids.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Amino acids are the constituent units of proteins and are therefore taken daily as part of one\u2019s diet. Individuals with Methylmalonic or Propionic Aciduria should follow a diet free from the amino acids involved in the pathology (methionine, threonine and valine) and should also take a reduced amount of the amino acid isoleucine.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Given the impossibility of excluding these amino acids from natural proteins, the patient should, in general, follow a protein-free diet, supplemented with adequate protein substitutes (not containing methionine, threonine and valine and with a low content of isoleucine). The treatment is, however, customized according to the individual patient&#8217;s protein needs.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">PIAM, always attentive to the problems related to rare or low-prevalence diseases, offers a diversified range of specific protein substitutes for the proper nutritional management of patients affected by Methylmalonic or Propionic Aciduria, providing tailor-made solutions for all ages, from infancy to adulthood.<\/span><\/p>\n","protected":false},"featured_media":3502,"template":"","categoria-patologia":[215],"class_list":["post-3501","patologia","type-patologia","status-publish","has-post-thumbnail","hentry","categoria-patologia-inborn-errors-of-protein-metabolism"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.7 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Methylmalonic Aciduria \/ Propionic Aciduria (MMA \/ PA) - PIAM farmaceutici s.p.a<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.piamfarmaceutici.com\/en\/patologia\/metilmalonico-aciduria-propionico-aciduria-mma-pa\/\" \/>\n<meta property=\"og:locale\" content=\"en_US\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Methylmalonic Aciduria \/ Propionic Aciduria (MMA \/ PA) - PIAM farmaceutici s.p.a\" \/>\n<meta property=\"og:description\" content=\"Methylmalonic Aciduria and Propionic Aciduria are hereditary metabolic diseases related to the metabolism of some amino acids. Amino acids are the constituent units of proteins and are therefore taken daily as part of one\u2019s diet. Individuals with Methylmalonic or Propionic Aciduria should follow a diet free from the amino acids involved in the pathology (methionine, [&hellip;]\" \/>\n<meta property=\"og:url\" content=\"https:\/\/www.piamfarmaceutici.com\/en\/patologia\/metilmalonico-aciduria-propionico-aciduria-mma-pa\/\" \/>\n<meta property=\"og:site_name\" content=\"PIAM farmaceutici s.p.a\" \/>\n<meta property=\"article:modified_time\" content=\"2023-01-27T11:49:43+00:00\" \/>\n<meta property=\"og:image\" content=\"https:\/\/www.piamfarmaceutici.com\/wp-content\/uploads\/2023\/01\/metilmalonico_aciduria_MMA_PA-1-4.jpg\" \/>\n\t<meta property=\"og:image:width\" content=\"1920\" \/>\n\t<meta property=\"og:image:height\" content=\"1280\" \/>\n\t<meta property=\"og:image:type\" content=\"image\/jpeg\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Est. reading time\" \/>\n\t<meta name=\"twitter:data1\" content=\"1 minute\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\\\/\\\/schema.org\",\"@graph\":[{\"@type\":\"WebPage\",\"@id\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/en\\\/patologia\\\/metilmalonico-aciduria-propionico-aciduria-mma-pa\\\/\",\"url\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/en\\\/patologia\\\/metilmalonico-aciduria-propionico-aciduria-mma-pa\\\/\",\"name\":\"Methylmalonic Aciduria \\\/ Propionic Aciduria (MMA \\\/ PA) - PIAM farmaceutici s.p.a\",\"isPartOf\":{\"@id\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/#website\"},\"primaryImageOfPage\":{\"@id\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/en\\\/patologia\\\/metilmalonico-aciduria-propionico-aciduria-mma-pa\\\/#primaryimage\"},\"image\":{\"@id\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/en\\\/patologia\\\/metilmalonico-aciduria-propionico-aciduria-mma-pa\\\/#primaryimage\"},\"thumbnailUrl\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/wp-content\\\/uploads\\\/2023\\\/01\\\/metilmalonico_aciduria_MMA_PA-1-4.jpg\",\"datePublished\":\"2023-01-09T16:22:44+00:00\",\"dateModified\":\"2023-01-27T11:49:43+00:00\",\"breadcrumb\":{\"@id\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/en\\\/patologia\\\/metilmalonico-aciduria-propionico-aciduria-mma-pa\\\/#breadcrumb\"},\"inLanguage\":\"en-US\",\"potentialAction\":[{\"@type\":\"ReadAction\",\"target\":[\"https:\\\/\\\/www.piamfarmaceutici.com\\\/en\\\/patologia\\\/metilmalonico-aciduria-propionico-aciduria-mma-pa\\\/\"]}]},{\"@type\":\"ImageObject\",\"inLanguage\":\"en-US\",\"@id\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/en\\\/patologia\\\/metilmalonico-aciduria-propionico-aciduria-mma-pa\\\/#primaryimage\",\"url\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/wp-content\\\/uploads\\\/2023\\\/01\\\/metilmalonico_aciduria_MMA_PA-1-4.jpg\",\"contentUrl\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/wp-content\\\/uploads\\\/2023\\\/01\\\/metilmalonico_aciduria_MMA_PA-1-4.jpg\",\"width\":1920,\"height\":1280},{\"@type\":\"BreadcrumbList\",\"@id\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/en\\\/patologia\\\/metilmalonico-aciduria-propionico-aciduria-mma-pa\\\/#breadcrumb\",\"itemListElement\":[{\"@type\":\"ListItem\",\"position\":1,\"name\":\"Home\",\"item\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/en\\\/\"},{\"@type\":\"ListItem\",\"position\":2,\"name\":\"Methylmalonic Aciduria \\\/ Propionic Aciduria (MMA \\\/ PA)\"}]},{\"@type\":\"WebSite\",\"@id\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/#website\",\"url\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/\",\"name\":\"PIAM farmaceutici s.p.a\",\"description\":\"\",\"potentialAction\":[{\"@type\":\"SearchAction\",\"target\":{\"@type\":\"EntryPoint\",\"urlTemplate\":\"https:\\\/\\\/www.piamfarmaceutici.com\\\/?s={search_term_string}\"},\"query-input\":{\"@type\":\"PropertyValueSpecification\",\"valueRequired\":true,\"valueName\":\"search_term_string\"}}],\"inLanguage\":\"en-US\"}]}<\/script>\n<!-- \/ Yoast SEO plugin. -->","yoast_head_json":{"title":"Methylmalonic Aciduria \/ Propionic Aciduria (MMA \/ PA) - PIAM farmaceutici s.p.a","robots":{"index":"index","follow":"follow","max-snippet":"max-snippet:-1","max-image-preview":"max-image-preview:large","max-video-preview":"max-video-preview:-1"},"canonical":"https:\/\/www.piamfarmaceutici.com\/en\/patologia\/metilmalonico-aciduria-propionico-aciduria-mma-pa\/","og_locale":"en_US","og_type":"article","og_title":"Methylmalonic Aciduria \/ Propionic Aciduria (MMA \/ PA) - PIAM farmaceutici s.p.a","og_description":"Methylmalonic Aciduria and Propionic Aciduria are hereditary metabolic diseases related to the metabolism of some amino acids. Amino acids are the constituent units of proteins and are therefore taken daily as part of one\u2019s diet. Individuals with Methylmalonic or Propionic Aciduria should follow a diet free from the amino acids involved in the pathology (methionine, [&hellip;]","og_url":"https:\/\/www.piamfarmaceutici.com\/en\/patologia\/metilmalonico-aciduria-propionico-aciduria-mma-pa\/","og_site_name":"PIAM farmaceutici s.p.a","article_modified_time":"2023-01-27T11:49:43+00:00","og_image":[{"width":1920,"height":1280,"url":"https:\/\/www.piamfarmaceutici.com\/wp-content\/uploads\/2023\/01\/metilmalonico_aciduria_MMA_PA-1-4.jpg","type":"image\/jpeg"}],"twitter_card":"summary_large_image","twitter_misc":{"Est. reading time":"1 minute"},"schema":{"@context":"https:\/\/schema.org","@graph":[{"@type":"WebPage","@id":"https:\/\/www.piamfarmaceutici.com\/en\/patologia\/metilmalonico-aciduria-propionico-aciduria-mma-pa\/","url":"https:\/\/www.piamfarmaceutici.com\/en\/patologia\/metilmalonico-aciduria-propionico-aciduria-mma-pa\/","name":"Methylmalonic Aciduria \/ Propionic Aciduria (MMA \/ PA) - PIAM farmaceutici s.p.a","isPartOf":{"@id":"https:\/\/www.piamfarmaceutici.com\/#website"},"primaryImageOfPage":{"@id":"https:\/\/www.piamfarmaceutici.com\/en\/patologia\/metilmalonico-aciduria-propionico-aciduria-mma-pa\/#primaryimage"},"image":{"@id":"https:\/\/www.piamfarmaceutici.com\/en\/patologia\/metilmalonico-aciduria-propionico-aciduria-mma-pa\/#primaryimage"},"thumbnailUrl":"https:\/\/www.piamfarmaceutici.com\/wp-content\/uploads\/2023\/01\/metilmalonico_aciduria_MMA_PA-1-4.jpg","datePublished":"2023-01-09T16:22:44+00:00","dateModified":"2023-01-27T11:49:43+00:00","breadcrumb":{"@id":"https:\/\/www.piamfarmaceutici.com\/en\/patologia\/metilmalonico-aciduria-propionico-aciduria-mma-pa\/#breadcrumb"},"inLanguage":"en-US","potentialAction":[{"@type":"ReadAction","target":["https:\/\/www.piamfarmaceutici.com\/en\/patologia\/metilmalonico-aciduria-propionico-aciduria-mma-pa\/"]}]},{"@type":"ImageObject","inLanguage":"en-US","@id":"https:\/\/www.piamfarmaceutici.com\/en\/patologia\/metilmalonico-aciduria-propionico-aciduria-mma-pa\/#primaryimage","url":"https:\/\/www.piamfarmaceutici.com\/wp-content\/uploads\/2023\/01\/metilmalonico_aciduria_MMA_PA-1-4.jpg","contentUrl":"https:\/\/www.piamfarmaceutici.com\/wp-content\/uploads\/2023\/01\/metilmalonico_aciduria_MMA_PA-1-4.jpg","width":1920,"height":1280},{"@type":"BreadcrumbList","@id":"https:\/\/www.piamfarmaceutici.com\/en\/patologia\/metilmalonico-aciduria-propionico-aciduria-mma-pa\/#breadcrumb","itemListElement":[{"@type":"ListItem","position":1,"name":"Home","item":"https:\/\/www.piamfarmaceutici.com\/en\/"},{"@type":"ListItem","position":2,"name":"Methylmalonic Aciduria \/ Propionic Aciduria (MMA \/ PA)"}]},{"@type":"WebSite","@id":"https:\/\/www.piamfarmaceutici.com\/#website","url":"https:\/\/www.piamfarmaceutici.com\/","name":"PIAM farmaceutici s.p.a","description":"","potentialAction":[{"@type":"SearchAction","target":{"@type":"EntryPoint","urlTemplate":"https:\/\/www.piamfarmaceutici.com\/?s={search_term_string}"},"query-input":{"@type":"PropertyValueSpecification","valueRequired":true,"valueName":"search_term_string"}}],"inLanguage":"en-US"}]}},"_links":{"self":[{"href":"https:\/\/www.piamfarmaceutici.com\/en\/wp-json\/wp\/v2\/patologia\/3501","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.piamfarmaceutici.com\/en\/wp-json\/wp\/v2\/patologia"}],"about":[{"href":"https:\/\/www.piamfarmaceutici.com\/en\/wp-json\/wp\/v2\/types\/patologia"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/www.piamfarmaceutici.com\/en\/wp-json\/wp\/v2\/media\/3502"}],"wp:attachment":[{"href":"https:\/\/www.piamfarmaceutici.com\/en\/wp-json\/wp\/v2\/media?parent=3501"}],"wp:term":[{"taxonomy":"categoria-patologia","embeddable":true,"href":"https:\/\/www.piamfarmaceutici.com\/en\/wp-json\/wp\/v2\/categoria-patologia?post=3501"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}